Discussion
Diagnosis With Brief Discussion
- Diagnosis
- Poland syndrome
- Radiologic Findings
- Figs 1-3. Agenesis of Rt pectoralis muscle.
Atropic Rt breast
Fig 4. Aplastic distal phalanges of right 2nd-5th finger
short fingers with soft tissue webbing between fingers.
- Brief Review
- Uncommon congenital anomaly characterized by unilateral anomalies of the chest wall and upper extremity (Rt > Lt)
Sporadic, although rare familial cases have been described
Isolated vascular insult in early gestation (involving embryonic subclavian and vertebral arteries)
Aplasia or hypoplasia of
: Pectoralis major (most common), pectoralis minor, ipsilateral 2nd to 5th ribs,
ipsilateral breast or nipples + brachysyndactyly, simian crease of affected extremity
Radiologic findings
Plain radiography : unilateral hyperlucent hemithorax
CT or MRI : absence of the pectoralis muscles and other anomalies
- References
- Acta Radiol 2008; 49: 387
- Please refer to
- Case 1031 Case 490
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- Keywords
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